[A case report of Kasabach-Merritt syndrome].
نویسندگان
چکیده
Kasabach Merritt syndrome (KMS) is an uncommon complication of large haemangioma in which there is thrombocytopenia and coagulopathy. We report a case of a new born male baby presented with a large haemangioma on the right upper extremity and his initial laboratory tests were consistent with consumptive coagulopathy. He was diagnosed as a case of KMS and treated with oral prednisolone. 1. Associate professor, Paediatric Department, Jalalabad Ragib Rabeya Medical College. 2. IMO, Paediatric Department, Jalalabad Ragib Rabeya Medical College. 3. Asst. Registrar, Paediatric Department, Jalalabad Ragib Rabeya Medical College. Correspondence: Dr. Tahmina Jahan Choudhury, Email : [email protected] Case Report: A new born male baby, first issue of his nonconsanguineous parents presented with a large sized hemangioma on his right upper extremity and small hemangioma on the neck and on parietal region of the scalp. Baby was born before term at 30th weeks of gestation by LUCS due to pre-mature rupture of the membrane. His mother was 25 year-old-lady with good general health and was on regular antenatal checkup. There was no family history of similar illness. On examination baby was pre term, very low birth weight 1.25kg with large, solitary 20cmX10cm sized erythematous induration on the right upper extremity. Two other indurations were noted on the neck (3x2cm sized) and parietal region of the scalp (2x1cm sized). These lesions were diagnosed as hemangioma. The initial laboratory data revealed normocytic normochromic anaemia(Hb% 10.5gm/dl), thrombocytopenia (Platelet count 80,000/cumm of blood). Other laboratory results including WBC counts, bleeding time, clotting time, activated partial thromboplastin time (APTT), prothombin time were within the normal range. Patient was diagnosed as Kasabach Merritt syndrome from a pre-existing hemangioma, clinical findings and laboratory values. Baby was managed with blood transfusion and oral prednisolone. Seven days after initiating treatment his platelet count was increased and lesion ceased to expand. Then dose of the prednisolone was subsequently tapered. BANGLADESH J CHILD HEALTH 2012; VOL 36 (2) : 105-107 .
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ورودعنوان ژورنال:
- Zhongguo dang dai er ke za zhi = Chinese journal of contemporary pediatrics
دوره 8 3 شماره
صفحات -
تاریخ انتشار 2006